Craniosynostosis, Dandy-Walker Variant (DWv) and Arnold-Chiari Malformations — Signs and Symptoms

These are a group of congenital malformations that involve the cranial cavity and the central nervous system.The Dandy-Walker variant is the commonest posterior fossa malformation, while craniosynostosis is the premature fusion of one or more of the cranial sutures causing abnormal shape of the head. They present with hydrocephalus and features of increased intracranial pressure, thus, the goal of therapy is to relieve the pressure. The main modalities of treatment are surgical interventions either endoscopically or under direct vision via scalp incisions.